Right Atrial Fibrosarcoma Mimicking Myxoma with Intermittent Complete Atrioventricular Block in a Young Adult: A Case Report

Authors

  • Hendrajat Parmana Putra General Practitioner, Abdoel Wahab Sjahranie General Hospital, Samarinda, Indonesia
  • Annisa Nurul Huda Jayanty Intervention Cardiologist, Abdoel Wahab sjahranie General Hospital, Samarinda, Indonesia
  • Djoen Herdianto Intervention Cardiologist, Abdoel Wahab sjahranie General Hospital, Samarinda, Indonesia
  • Diah Purwandini Asmoro Intervention Cardiologist, Abdoel Wahab sjahranie General Hospital, Samarinda, Indonesia

DOI:

https://doi.org/10.55681/armada.v4i10.4941

Keywords:

Right Atrial Tumor, Cardiac Myxoma, Cardiac Fibrosarcoma, Atrioventricular Block, Permanent Pacemaker, Ventricular Fibrillation

Abstract

Primary cardiac tumors are rare and may be associated with nonspecific symptoms and cardiac conduction disturbances. Preoperative imaging may not reliably distinguish benign from malignant cardiac masses. A 19-year-old man presented with progressive dyspnea, fatigue, and diaphoresis. Electrocardiographic assessment identified first-degree atrioventricular (AV) block with intermittent complete AV block. Transthoracic echocardiography revealed a 2 × 2 cm right atrial mass with a left ventricular ejection fraction of 65%, and cardiac computed tomography raised suspicion of myxoma. While awaiting surgery, the patient received dopamine at 15 μg/kg/min and oxygen at 3 L/min by nasal cannula. He underwent tumor excision with cardiopulmonary bypass and permanent pacemaker implantation. Intraoperative ventricular fibrillation caused cardiac arrest, for which defibrillation and adrenaline were administered. Histopathology was reported as low-grade fibrosarcoma. After three days of intensive care, he was discharged in stable condition on postoperative day four. A right atrial tumor clinically suspected to be myxoma was associated with advanced intermittent AV conduction disease and was subsequently reported as low-grade fibrosarcoma. This case emphasizes cardiac imaging, rhythm surveillance, histopathological assessment, and careful interpretation of perioperative outcomes.

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References

Angeli, F., Bodega, F., Bergamaschi, L., Armillotta, M., Amicone, S., Canton, L., Fedele, D., Suma, N., Cavallo, D., Foà, A., Belmonte, M., Russo, V., Attinà, D., Niro, F., Bonfiglioli, R., Fanti, S., Pavon, A. G., Guglielmo, M., Mushtaq, S., ... Pizzi, C. (2024). Multimodality imaging in the diagnostic work-up of patients with cardiac masses: JACC: CardioOncology state-of-the-art review. JACC: CardioOncology, 6(6), 847–862. https://doi.org/10.1016/j.jaccao.2024.09.006

Davila, C. D., Slipczuk, L., & Pressman, G. S. (2014). Right atrial lipoma in a patient with complete heart block. Journal of Medical Cases, 5(5), 270–272. https://doi.org/10.14740/jmc1746w

Kabashi, S., Hoxha, N., Gashi, S., Ahmegjekaj, I., Bejta, I., Sadiku, M., Ymeri, H., Kabashi, A., Bicaj, X., & Mucaj, S. (2013). Primary fibro sarcoma of the heart. Acta Informatica Medica, 21(3), 213–215. https://doi.org/10.5455/aim.2013.21.213-215

Kusumoto, F. M., Schoenfeld, M. H., Barrett, C., Edgerton, J. R., Ellenbogen, K. A., Gold, M. R., Goldschlager, N., Hamilton, R. M., Joglar, J. A., Kim, R. J., Lee, R., Marine, J. E., McLeod, C. J., Oken, K. R., Patton, K. K., Pellegrini, C. N., Selzman, K. A., Thompson, A., & Varosy, P. D. (2019). 2018 ACC/AHA/HRS guideline on the evaluation and management of patients with bradycardia and cardiac conduction delay. Journal of the American College of Cardiology, 74(7), e51–e156. https://doi.org/10.1016/j.jacc.2018.10.044

Muthiah, R. (2016). Right atrial myxoma: A case report. Case Reports in Clinical Medicine, 5(3), 101–106. https://doi.org/10.4236/crcm.2016.53013

Rabiee Rad, M., Ghasempour Dabaghi, G., Darouei, B., Amani-Beni, R., Zare, M. M., Shirin, F., & Jamalian, M. (2024). Clinical and laboratory manifestations, ECG findings, and outcomes of right atrial myxoma: A systematic review of cases reported worldwide. The Egyptian Heart Journal, 76(1), Article 125. https://doi.org/10.1186/s43044-024-00550-x

Reynen, K. (1996). Frequency of primary tumors of the heart. The American Journal of Cardiology, 77(1), 107. https://doi.org/10.1016/S0002-9149(97)89149-7

Roberts, D. H., & Ramsdale, D. R. (1990). First degree atrioventricular block associated with right atrial myxoma. Postgraduate Medical Journal, 66(772), 140–141. https://doi.org/10.1136/pgmj.66.772.140

Silverman, N. A. (1980). Primary cardiac tumors. Annals of Surgery, 191(2), 127–138. https://doi.org/10.1097/00000658-198002000-00001

Willey, R. F., Matthews, M. B., & Walbaum, P. R. (1980). An unusual case of large right atrial myxoma. British Heart Journal, 44(1), 108–110. https://doi.org/10.1136/hrt.44.1.108

Yamada, A., Miyawaki, I., & Mima, H. (2022). Anesthetic management of primary cardiac tumor in the coronary sinus and right atrium. Saudi Journal of Anaesthesia, 16(4), 488–490. https://doi.org/10.4103/sja.sja_130_22

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Published

2026-10-31

How to Cite

Putra, H. P., Jayanty, A. N. H., Herdianto, D., & Asmoro, D. P. (2026). Right Atrial Fibrosarcoma Mimicking Myxoma with Intermittent Complete Atrioventricular Block in a Young Adult: A Case Report. ARMADA : Jurnal Penelitian Multidisiplin, 4(10), 7208–7213. https://doi.org/10.55681/armada.v4i10.4941